How to eat right in patients with hepatolenticular degeneration

Our reporter Wu Xueqin correspondent Huang Fangming

Hepatolenticular degeneration (WD) is a rare autosomal recessive disorder of copper metabolism (copper deposition in tissues and organs) caused by mutations in the ATP7B gene located on chromosome 13

Wang Qifan, deputy chief physician of the Department of Pediatrics at the First Hospital of Quanzhou City, Fujian Province, said that patients with hepatolenticular degeneration are treatable

Diet therapy is a necessary means to treat hepatolenticular degeneration.

low copper diet

It is forbidden to use copper cookware and utensils to cook food

Increase intake of foods high in zinc, manganese, molybdenum, protein, vitamins

Increase the intake of B vitamin foods, especially foods containing vitamin B6, such as green vegetables, cabbage, etc.

Increase high-quality protein intake to protect liver function

The breakdown products of protein amino acids can promote copper excretion

reduce fat intake

Most patients with hepatolenticular degeneration have lipid metabolism disorders, so they should control fat intake and eat less fatty meat

calcium supplement

Milk is the first choice for calcium supplementation in patients with hepatolenticular degeneration

diet care

　　While giving dietary treatment, attention should be paid to avoid foods that excite the nervous system, such as strong tea, coffee, broth, chicken soup, etc.

　　Wang Qifan, Deputy Chief Physician of the Department of Pediatrics of the First Hospital of Quanzhou City, Fujian Province, Executive Director of the Pediatric Branch of the Fujian Strait Medicine and Health Exchange Association, Member and Secretary of the Neonatal Group of the Pediatric Branch of the Fujian Medical Association, and Executive Director of the Quanzhou Pediatric Society

        "China Food News" (April 21, 2021 03 edition)

(Editor-in-charge: Zhou Yan)